Von Recklinghausen's disease with urogenital manifestation.

نویسندگان

  • Thiago F Nunes
  • Renato P Costa
  • Fabio C Navarro
چکیده

Neurofibromatosis or Von Recklinghausen's disease is a rare disease that affects the urogenital system in its visceral form. We report on one case where the patient had a recurring mass located in the vesicouterine space that caused irritative urinary symptoms, which was confirmed as uterine cervix neurofibroma following surgery and immunohistochemical study. We stress the importance of a wide resection of such tumors and the need for long-term follow-up due to the high recurrence index and the risk of malignant transformation.

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Spontaneous haemothorax: a cause of sudden death in von Recklinghausen's disease.

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عنوان ژورنال:
  • International braz j urol : official journal of the Brazilian Society of Urology

دوره 31 2  شماره 

صفحات  -

تاریخ انتشار 2005